目的 探讨腹部副神经节瘤（PGL）患者的临床病理特征及长期预后分析。方法 对相关病 例数据库进行回顾性检索，分析腹部 PGL 患者的临床病理特征和长期随访预后，应用 Kaplan⁃Meier 法 进行生存分析，探讨腹部 PGL 术后复发及死亡的影响因素。结果 共纳入 24 例患者，平均年龄 58.9 岁，肿 瘤平均大小5 cm，主要位于肾下极以下。平均随访时间为54月。所有转移的患者肾上腺嗜铬细胞瘤评分 （PASS）≥ 4 分。1 例患者出现同步转移，2 例出现局部复发和远处转移。1 例患者在诊断 9 年后死亡。经 Kaplan⁃Meier 曲线分析显示，PASS 评分 4 ~ 7 分的患者复发或死亡的进展曲线明显高于 PASS 评分 0 ~ 3 分 的患者（P = 0.03）。结论 腹部 PGL 是一种罕见且预后良好的肿瘤。然而，其复发风险高，因此长期随访十分重要，尤其是对于PASS ≥ 4分的患者。

Objective To investigate the clinicopathological features and long ⁃term outcomes of patients with abdominal paraganglioma（PGL）. Methods A retrospective study of relevant databases were performed to analyze theclinicopathological features and long⁃term follow⁃up outcomes of patients with abdominal PGL. Kaplan⁃ Meier survival analysis was performed to explore the influencing factors of postoperative recurrence or death of abdominal PGL. Results A total of 24 patients were confirmed with abdominal PGL. The average age of diagnosis was 58.9 years. The average tumor size was 5 cm and they were predominantly located in the infrarenal position. The mean follow⁃up period was 54 months. All patients with metastases had pheochromocytoma of the Adrenal Gland Scaled Score（PASS）of ≥ 4. One patient presented with synchronous metastases while 2 developed local recurrence and distant metastases. One patient died 9 years after diagnosis. Kaplan⁃Meier curve analysis showed recurrence or death in patients with PASS score of 4 ~ 7 was significantly higher than patients with PASS score of 0 ~ 3（P = 0.03）. Conclusions Abdominal PGL is a rare tumor with excellent long⁃term prognosis. Recurrence， although common，can occur decades after initial diagnosis. Long⁃term follow⁃up is therefore recommended for all patients with PGL，especially in patients with PASS of ≥ 4.